Rhabdomyosarcoma is a highly aggressive and the most common soft tissue sarcoma inn children. Sites of involvement include the orbit, the nose, the paranasal sinuses, the oropharynx, soft tissue, the nasopharynx, and the external ear or mastoid ;
however, the nasal vestibule, in particular, is an uncommon site. Rhabdomyosarcoma in the nasal vestibule has been reported in only one case in the literature so far and has never been reported in Korea. We experienced a case of embryonal
rhabdomyosarcoma of the nasal vestibule which was managed with total excision of tumor mass and chemotherapy. We report the case and discuss the therapy and management of this unusual problem.
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